Scimitar Syndrome: Fundamental Characteristics and Perioperative Anesthesia Considerations
We present to you the case of a 5-week-old male with Scimitar syndrome. Patient was born prematurely and was admitted to NICU due to respiratory distress, impaired thermoregulation, and hyperbilirubinemia which normalized eventually. Sepsis work-up was negative. However, his CXR showed significant volume loss on the right side, rightward mediastinal shift, and a bandlike opacity. A chest CT with contrast and echocardiogram were obtained that ultimately confirmed Scimitar syndrome with the following complications: Horseshoe lung, two anomalous pulmonary veins, right lung hypoplasia, and cardiac dextroposition. We will discuss the fundamental characteristics of this syndrome and perioperative anesthesia considerations.
Haider N, Donatelli D, Asbahi MF. Scimitar syndrome: fundamental characteristics and perioperative anesthesia considerations. Presented at: American Society of Anesthesiologists Annual Meeting; 2023 Oct 15; San Francisco, CA.