Scimitar Syndrome: Fundamental Characteristics and Perioperative Anesthesia Considerations

Document Type

Conference Proceeding

Publication Date



We present to you the case of a 5-week-old male with Scimitar syndrome. Patient was born prematurely and was admitted to NICU due to respiratory distress, impaired thermoregulation, and hyperbilirubinemia which normalized eventually. Sepsis work-up was negative. However, his CXR showed significant volume loss on the right side, rightward mediastinal shift, and a bandlike opacity. A chest CT with contrast and echocardiogram were obtained that ultimately confirmed Scimitar syndrome with the following complications: Horseshoe lung, two anomalous pulmonary veins, right lung hypoplasia, and cardiac dextroposition. We will discuss the fundamental characteristics of this syndrome and perioperative anesthesia considerations.


American Society of Anesthesiologists Annual Meeting, October 12-16, 2023, San Francisco, CA