Peripheral Nerve Sheath Tumors of the Orbit

Chapter Title

Peripheral Nerve Sheath Tumors of the Orbit

Book Title

Albert and Jakobiec's Principles and Practice of Ophthalmology

Files

Editors

Albert, Daniel , Miller, Joan , Azar, Dimitri , Young, Lucy H.

Description

Peripheral nerve sheath tumors (PNSTs) are neoplasms that arise from peripheral nerves or demonstrate nerve sheath differentiation. They usually present with proptosis and sometimes with severe periocular deformities. Benign PNST subtypes, including schwannomas and neurofibromas, are more common than rare malignant forms and are known to occur in the orbit and ocular adnexa. PNSTs comprise approximately 4% of all orbital tumors.

First Page

1

Last Page

46

ISBN

9783319904955

Publication Date

2021

Publisher

Springer

City

Cham

Keywords

Schwannoma, Astrocytoma, Glioma, Neurofibroma, Meningioma, Neurofibromatosis, Neuroblastoma, Optic nerve, Multiple endocrine neoplasia, Orbital embryology

Disciplines

Ophthalmology

Peripheral Nerve Sheath Tumors of the Orbit

Share

COinS