Peripheral Nerve Sheath Tumors of the Orbit
Book Title
Albert and Jakobiec's Principles and Practice of Ophthalmology
Files
Editors
Albert, Daniel , Miller, Joan , Azar, Dimitri , Young, Lucy H.
Description
Peripheral nerve sheath tumors (PNSTs) are neoplasms that arise from peripheral nerves or demonstrate nerve sheath differentiation. They usually present with proptosis and sometimes with severe periocular deformities. Benign PNST subtypes, including schwannomas and neurofibromas, are more common than rare malignant forms and are known to occur in the orbit and ocular adnexa. PNSTs comprise approximately 4% of all orbital tumors.
First Page
1
Last Page
46
ISBN
9783319904955
Publication Date
2021
Publisher
Springer
City
Cham
Keywords
Schwannoma, Astrocytoma, Glioma, Neurofibroma, Meningioma, Neurofibromatosis, Neuroblastoma, Optic nerve, Multiple endocrine neoplasia, Orbital embryology
Disciplines
Ophthalmology
Recommended Citation
Carniciu A, Kahana A, Levin LA. Peripheral Nerve Sheath Tumors of the Orbit In: Albert D, Miller J, Azar D, Young LH, editors. Albert and Jakobiec's Principles and Practice of Ophthalmology. [Internet]. Cham: Springer International Publishing; 2020 p. 1-46. Available from: https://doi.org/10.1007/978-3-319-90495-5_65-1 DOI: 10.1007/978-3-319-90495-5_65-1