Spinal Epidural Venous Plexus Pathology in Hirayama Disease.

Document Type

Article

Publication Date

9-1-2019

Publication Title

Journal of Clinical Neuromuscular Disease

Abstract

Hirayama disease is a rare juvenile amyotrophy that is often misdiagnosed as an unrelated, relentlessly progressive disease. We present the case of an 18-year-old man who presented with weakness and atrophy of the right forearm and hand. Dynamic cervical magnetic resonance imaging was used, revealing the classic findings of epidural venous plexus dilation and anterior displacement of the dural sac. In addition, dilation of the external vertebral venous plexus was visualized. We discuss the clinical utility of dynamic magnetic resonance imaging and the underlying pathophysiology of these findings in Hirayama disease.

Volume

21

Issue

1

First Page

47

Last Page

51

DOI

10.1097/CND.0000000000000243

ISSN

1537-1611

PubMed ID

31453855

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