"Arrhythmogenic Right Ventricular Cardiomyopathy Presenting With VT Ele" by Shon Thomas, Jaclynn Jackubowski et al.
 

Arrhythmogenic Right Ventricular Cardiomyopathy Presenting With VT Electrical Storm.

Document Type

Article

Publication Date

1-6-2025

Publication Title

Journal of community hospital internal medicine perspectives

Abstract

Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) is a right ventricular disease caused by desmosomal gene mutations leading to fibro-fatty replacement of the myocardium causing ventricular arrhythmias such as ventricular tachycardia (VT). A 59-year-old female presented with new onset VT manifesting as shortness of breath and chest discomfort. Diagnostic workup revealed right ventricular dilation/dysfunction on echocardiogram, VT with left bundle branch block (LBBB) and diffuse T wave inversions (TWIs) on EKG. She was discharged with a diagnosis of ARVC. Later, she developed VT storm, treated with epi-endocardial ablation for complete resolution of recurrent VT. Our case demonstrates the rare presentation of ARVC as ventricular storm and the various management strategies such as anti-arrhythmics, automated implantable cardioverter-defibrillator (AICD) and ablation procedures.

Volume

15

Issue

1

First Page

70

Last Page

74

DOI

10.55729/2000-9666.1432

ISSN

2000-9666

PubMed ID

39867147

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