"Granulomatous Lymphocyte Interstitial Lung Disease: A Rare Complicatio" by Ali Khreisat, Vickie Xin et al.
 

Granulomatous Lymphocyte Interstitial Lung Disease: A Rare Complication of Common Variable Immunodeficiency Managed With Azathioprine and Rituximab.

Document Type

Article

Publication Date

4-30-2024

Publication Title

Cureus

Abstract

Granulomatous lymphocytic interstitial lung disease (GL-ILD) is a rare, non-infectious pulmonary manifestation of common variable immunodeficiency (CVID). Diagnosing and managing GLILD remains challenging due to its poorly understood pathogenesis and high mortality. We present a complex case of a young female with CVID associated with lung and spinal cord involvement managed with azathioprine and rituximab.

Volume

16

Issue

4

First Page

e59399

DOI

10.7759/cureus.59399

ISSN

2168-8184

PubMed ID

38689676

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