Risk Of Massive Hemorrhage In Pediatric Patients With Pheochromocytoma

Authors

Luu Pham, Oakland University William Beaumont School of Medicine Medical Student
Sheridan Nicole Markatos, Beaumont Health Resident
Nathan Novotny, Beaumont Health
roy G. Soto, Beaumont Health

Document Type

Conference Proceeding

Publication Date

10-24-2022

Abstract

We present a case of an 11-year-old male with a family history of von Hippel-Lindau (VHL) syndrome and pheochromocytoma who had persistent asymptomatic hypertension. Further evaluations at the hospital revealed a 5.9-cm right adrenal mass, genetic test confirming VHL and positive urine metanephrines. Given the high likelihood of pheochromocytoma, he underwent a laparoscopic unilateral adrenalectomy with pre-operative administration of phenoxybenzamine. The surgery was converted to open due to significant hemorrhage following a right adrenal vein division. We discuss the pathophysiology of VHL, risk factors and perioperative management strategies for massive blood loss during surgery in pediatric population with pheochromocytoma.

Comments

American Society of Anesthesiology Annual Meeting, New Orleans, LA, October 21-25, 2022.

Recommended Citation

Pham L, Markatos S, Novotny N, Soto R. Risk of massive hemorrhage in pediatric patients with pheochromocytoma. Presented at: American Society of Anesthesiology Annual Meeting; 2022 Oct 21-25; New Orleans, LA.