Risk Of Massive Hemorrhage In Pediatric Patients With Pheochromocytoma

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Conference Proceeding

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We present a case of an 11-year-old male with a family history of von Hippel-Lindau (VHL) syndrome and pheochromocytoma who had persistent asymptomatic hypertension. Further evaluations at the hospital revealed a 5.9-cm right adrenal mass, genetic test confirming VHL and positive urine metanephrines. Given the high likelihood of pheochromocytoma, he underwent a laparoscopic unilateral adrenalectomy with pre-operative administration of phenoxybenzamine. The surgery was converted to open due to significant hemorrhage following a right adrenal vein division. We discuss the pathophysiology of VHL, risk factors and perioperative management strategies for massive blood loss during surgery in pediatric population with pheochromocytoma.


American Society of Anesthesiology Annual Meeting, New Orleans, LA, October 21-25, 2022.